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NEUROLOGY 2004;63:176-178
© 2004 American Academy of Neurology
Brief Communications

Ventilatory support in facioscapulohumeral muscular dystrophy

M. Wohlgemuth, MD, E. L. van der Kooi, MD, R. G. van Kesteren, MD PhD, S. M. van der Maarel, PhD and G. W. Padberg, MD PhD

From the Department of Neurology (Drs. Wohlgemuth, van der Kooi, and Padberg), University Medical Center Nijmegen, Center for Home Mechanical Ventilation (Dr. van Kesteren), University Medical Center Utrecht, and Center for Human Clinical Genetics (Dr. van der Maarel), Leiden University Medical Center, the Netherlands.

Address correspondence and reprint requests to Dr. M Wohlgemuth, Department of Neurology, University Medical Center Nijmegen, Reinier Postlaan 4, 6500 HB Nijmegen, the Netherlands; e-mail: m.wohlgemuth{at}neuro.umcn.nl

Respiratory insufficiency due to respiratory muscle weakness is a common complication of many neuromuscular diseases. The prevalence of respiratory failure in facioscapulohumeral muscular dystrophy (FSHD) is unknown. The authors identified 10 FSHD patients on nocturnal ventilatory support at home, representing approximately 1% of the Dutch FSHD population. Severe muscle disease, wheelchair dependency, and kyphoscoliosis appeared to be risk factors for respiratory failure.

Received October 1, 2003. Accepted in final form February 27, 2004.




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Correspondence:

Read all Correspondence

Ventilatory support in facioscapulohumeral muscular dystrophy
Gregory T Carter, et al.
Neurology Online, 2 Sep 2004 [Full text]
Reply to Bird et al
Marielle Wohlgemuth
Neurology Online, 15 Sep 2004 [Full text]

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