Measuring Friedreich ataxia: Interrater reliability of a neurologic rating scale
Abstract
Measuring the severity of neurologic dysfunction in patients with inherited ataxias, including Friedreich ataxia (FA), is difficult because of the variable rate of progression, the variable age at onset and the variety of neural systems that may be affected. The authors discuss the problems related to rating scales in the ataxias, report a neurologic rating scale for FA, and demonstrate acceptable interrater reliability of the instrument.
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Published online: April 11, 2005
Published in print: April 12, 2005
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